Assessment of Safety and Acute Effects of a Knee-hip Powered Soft Exoskeleton in Patients With Neuromuscular Disorders

Inclusion Criteria: * 18 years and \< 70 years of age * Height between 1.50 m and 1.95 m * Weight between 45 kg and 110 kg * Abdominal perimeter \< 125 cm * Written informed consent * Affiliate or beneficiary of a social security scheme * Able to comply with all protocol requirements * Confirmed diagnosis of a pathology belonging to one of the following family\*: * Primary disorders of muscles * Muscular dystrophy * Congenital myopathies * Idiopathic inflammatory myopathy * Mitochondrial myopathies * Metabolic disorders * Inborn errors of metabolism * Glycogen storage disease * Functional capacities: * Able to stand up from a chair with armrest without other supports at least 3 times and at most 15 times in 30 seconds. * Report the ability to walk without the assistance of a person at least 2min * The use of traditional orthoses and walking aids will be accepted excepted knee orthoses and walkers (e.g. canes/crutches, ankle foot orthosis). Exclusion Criteria: * Unable to participate in the study * Inability to comply with protocol requirements * Guardianship/trusteeship * Pregnant or nursing women * Unstable Cardiomyopathy * Symptomatic orthostatic hypotension * Medical history of osteoporotic fracture * Balance disorder with extra neuromuscular causes * Recent trauma (fall, accident, ...) * Unstable Cardiomyopathy * Severe respiratory insufficiency * Flexion contracture in the knee and hip joint in excess of 10° * Varus malposition in exc…