Evaluation of a Cohort of Congenital Deep Deafness Patients and/or With Auditory Neuropathy, Looking for DFNB9

G1a / Inclusion Criteria: * Child from 0 to 3 years old * Child with severe to profound bilateral deafness newly diagnosed with: * Average hearing threshold\> 70 decibel on each ear * and / or no response to 70 decibel PEA on each ear * and / or no response to ASSR G1b / Inclusion Criteria: * Child under 16 * Child with newly diagnosed hearing neuropathy : tonal/vocal dissociation (when this is possible), and/or modified PEA, and/or discordant ASSR, and/or OEA present. G2 / Inclusion Criteria: * Adult patient under 25 or child * Patient with deafness with auditory neuropathy * Patient known to have 1 or 2 mutations of the otoferlin protein Exclusion Criteria: * Other type of deafness such as : unilateral deafness, deafness of transmission, malformation syndrome, known genetic familial deafness not DFNB9 * Patient without medical insurance * Lack of consent to DNA sampling, of one or both biological parents (consent of the care)