The primary objective of the study is to perform 2-year follow up with motor parameters evolution using instrumental assessments in patients with limb girdle muscular dystrophie, and to identify which motor parameters are sensitive to change. The secondary objectives of the study are: * to describe the changes of the parameters obtained from instrumental evaluations in comparison with the changes obtained from clinical assessments. * to characterize the muscular impairments, the biomechanical gait disorders, the standing postural control disorders, the biomechanical upper limb disorders in spatial exploration, the limitation of upper limb capacities, the fatigue, the endurance, the patients' participation to their activities and their quality of life, in comparison with a healthy paired population. * to highlight the relationships between muscular assessment parameters, biomechanical gait parameters, standing posture control and upper limb spatial exploration. * to highlight the relationships between data from instrumental assessments and data from clinical assessments. * to highlight the relationships between instrumental assessments data and clinical assessments data on one side, and features of patients (age, sex, duration since diagnosis, type of LGMD, rehabilitation in follow-up, sportive practices...) on the other side.
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Change from baseline on maximal strength
Timeframe: Assessed at 6 months, 12 months, 18 months and 24 months
Change from baseline on peak hip flexion
Timeframe: Assessed at 6 months, 12 months, 18 months and 24 months
Change from baseline on speed of center of pression during standing postural control
Timeframe: Assessed at 6 months, 12 months, 18 months and 24 months
Change from baseline on elbow peak extension during upper limb spatial exploration
Timeframe: Assessed at 6 months, 12 months, 18 months and 24 months