Prospective, longitudinal, interventional, single-group, multicenter natural history study to better know the LGMD2I disease physiopathology. The duration of participation for each patient will be up to 24 months.
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6-Minute Walk Test
Timeframe: Baseline through 24 months
10-Meter Walk test (10MWT)
Timeframe: Baseline through 24 months
Timed Up and Go (TUG) test
Timeframe: Baseline through 24 months
Four-stair climb test
Timeframe: Baseline through 24 months
North Star Assessment for Neuromuscular Disorders (NSAD)
Timeframe: Baseline through 24 months
Upper limb assessment via the Performance of the Upper Limb (PUL) tool version 2.0
Timeframe: Baseline through 24 months
Recording of aids for ambulation
Timeframe: Baseline through 24 months
Isokinetic muscle testing using the Biodex System (optional)
Timeframe: Baseline through 24 months
Pulmonary function test
Timeframe: Baseline through 24 months
Electrocardiogram
Timeframe: Baseline through 24 months
Echocardiography
Timeframe: Baseline through 24 months